Anti-UPB1 antibody produced in rabbit

• Supplier: Sigma-Aldrich
• Catalog: HPA000728
• Prices: $429.00
• Sizes: 100 µl
• Host: Rabbit
• Clonality: Polyclonal
• Applications: IHC-P
• Species Reactivities: Human
• Antigen: β-Ureidopropionase recombinant protein epitope signature tag (PrEST)
• Description: Rabbit Polyclonal
• Gene: UPB1
• Conjugate: unconjugated

Product images

Immunohistochemistry
Anti-UPB1: Cat. No. HPA000728: Immunoperoxidase staining of formalin-fixed, paraffin-embedded human liver tissue showing cytoplasmic and/or membranous staining of hepatocytes.

Immunoblotting
Anti-UPB1: Cat. No. HPA000728:
Lanes
1. Marker [kDa] 250, 130, 95, 72, 55, 36, 28, 17, 10
2. Negative control (vector only transfected HEK293T lysate)
3. Over-expression lysate (Co-expressed with a C-terminal myc-DDK tag (~3.1 kDa) in mammalian HEK293T cells, LY414060)

Product References

ss-ureidopropionase deficiency: phenotype, genotype and protein structural - ss-ureidopropionase deficiency: phenotype, genotype and protein structural

van Kuilenburg AB, Dobritzsch D, Meijer J, Krumpel M, Selim LA, Rashed MS, Assmann B, Meinsma R, Lohkamp B, Ito T, Abeling NG, Saito K, Eto K, Smitka M, Engvall M, Zhang C, Xu W, Zoetekouw L, Hennekam RC. Biochim Biophys Acta. 2012 Jul;1822(7):1096-108. doi:

beta-Ureidopropionase deficiency: an inborn error of pyrimidine degradation - beta-Ureidopropionase deficiency: an inborn error of pyrimidine degradation

van Kuilenburg AB, Meinsma R, Beke E, Assmann B, Ribes A, Lorente I, Busch R, Mayatepek E, Abeling NG, van Cruchten A, Stroomer AE, van Lenthe H, Zoetekouw L, Kulik W, Hoffmann GF, Voit T, Wevers RA, Rutsch F, van Gennip AH. Hum Mol Genet. 2004 Nov 15;13(22):2793-801. Epub 2004 Sep 22.

Contribution of the beta-ureidopropionase (UPB1) gene alterations to the - Contribution of the beta-ureidopropionase (UPB1) gene alterations to the

Fidlerova J, Kleiblova P, Kormunda S, Novotny J, Kleibl Z. Pharmacol Rep. 2012;64(5):1234-42.

Genetic analysis of the first 4 patients with beta-ureidopropionase deficiency. - Genetic analysis of the first 4 patients with beta-ureidopropionase deficiency.

van Kuilenburg AB, Meinsma R, Assman B, Hoffman GF, Voit T, Ribes A, Lorente I, Busch R, Mayatepek E, Abeling NG, Wevers RA, Rutsch F, van Gennip AH. Nucleosides Nucleotides Nucleic Acids. 2006;25(9-11):1093-8.