Gene Symbol | BCKDHA |
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Entrez Gene | 102134149 |
Alt Symbol | BCKDE1A |
Species | Monkey |
Gene Type | protein-coding |
Description | branched chain keto acid dehydrogenase E1, alpha polypeptide |
Other Description | 2-oxoisovalerate dehydrogenase alpha subunit|2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial|BCKDH E1-alpha|Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain |
Swissprots | Q8HXY4 |
Accessions | Q8HXY4 AB083305 BAC20584 NM_001284089 NP_001271018 XM_005589354 XP_005589411 |
Function | The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). |
Subcellular Location | Mitochondrion matrix {ECO:0000250}. |
Top Pathways | Valine, leucine and isoleucine degradation |
Recombinant Macaca fascicularis 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial(BCKDHA) - CSB-YP812817MOV CSB-EP812817MOV CSB-BP812817MOV CSB-MP812817MOV from Cusabio
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2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (BCKDHA), Recombinant Protein - MBS1283211 from MyBioSource
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Recombinant Cynomolgus BCKDHA Protein, His-tagged - BCKDHA-338C from Creative Biomart
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