NEB

Gene Symbol NEB
Entrez Gene 4703
Alt Symbol NEB177D, NEM2
Species Human
Gene Type protein-coding
Description nebulin
Other Description nemaline myopathy type 2
Swissprots F8WCP0 Q53TG8 P20929 Q15346 F8WCL5 Q53QQ2
Accessions AAY14651 AAY14977 EAX11499 EAX11500 EAX11501 EAX11502 EAX11503 EAX11504 EAX11505 EAX11506 P20929 AK056994 BAB71337 AK093855 AK096887 BAG53391 AK096903 AK129532 AK300079 BAH13205 AK300674 BAH13324 AK300722 BAH13335 AK307607 BC012533 BC022421 AAH22421 BC029384 AAH29384 BC050436 AAH50436 BC056251 AAH56251 BC063136 AAH63136 BC105590 AAI05591 BP232190 BP233123 BX283647 BX648963 M19669 AAA59917 U35636 AAB02621 U35637 AAB02622 X58122 CAA41124 X83957 CAA58788 XM_005246590 XP_005246647 XM_005246591 XP_005246648 XM_005246592 XP_005246649 XM_005246593 XP_005246650 XM_005246594 XP_005246651 XM_005246595 XP_005246652 XM_005246596 XP_005246653 XM_005246597 XP_005246654 XM_005246598 XP_005246655 XM_005246599 XP_005246656 XM_005246600 XP_005246657 XM_005246601 XP_005246658 XM_005246602 XP_005246659 XM_005246603 XP_005246660 XM_005246604 XP_005246661 XM_005246606 XP_005246663 XM_005246608 XP_005246665 XM_005246610 XP_005246667 XM_005246611 XP_005246668 XM_005246612 XP_005246669 XM_005246613 XP_005246670 XM_005246615 XP_005246672 XM_005246616 XP_005246673 XM_005246617 XP_005246674 XM_006712541 XP_006712604 XM_006712542 XP_006712605 XM_011511224 XP_011509526 XM_011511225 XP_011509527 XM_011511226 XP_011509528 XM_011511227 XP_011509529 NM_001164507 NP_001157979 NM_001164508 NP_001157980 NM_001271208 NP_001258137 NM_004543 NP_004534
Function This giant muscle protein may be involved in maintaining the structural integrity of sarcomeres and the membrane system associated with the myofibrils. Binds and stabilize F-actin.
Subcellular Location Cytoplasm, myofibril, sarcomere. Cytoplasm, cytoskeleton.
Tissue Specificity Muscle specific. Located in the thin filament of striated muscle.

Nebulin (N-19) - sc-8083 from Santa Cruz Biotechnology

Prices $279.00
Sizes 200 µg/ml
Host Goat
Clonality Polyclonal
Nebulin (N-19): sc-8083. Immunoperoxidase staining of formalin fixed, paraffin-embedded human heart tissue showing cytoplasmic localization.

Nebulin (H-300) - sc-28286 from Santa Cruz Biotechnology

Prices $279.00
Sizes 200 µg/ml
Host Rabbit
Clonality Polyclonal
Nebulin (H-300): sc-28286. Immunofluorescence staining of normal mouse spleen frozen section showing cytoplasmic staining.

Nebulin (C-20) - sc-8082 from Santa Cruz Biotechnology

Prices $279.00
Sizes 200 µg/ml
Host Goat
Clonality Polyclonal

Anti-Nebulin antibody - ab199259 from Abcam

Prices $376.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal
Immunohistochemical analysis of paraffin-embedded Human lung cancer tissue labeling Nebulin with ab199259 at 1/80 dilution.

Anti-Nebulin antibody [NB2] - ab11099 from Abcam

Prices $370.00
Sizes 100 µl
Host Mouse
Clonality Monoclonal
Clone NB2

Anti-NEB / Nebulin Antibody - LS-C73206 from LifeSpan Bioscience

Prices $530.00
Sizes 100 µl
Host Mouse
Clonality Monoclonal

Anti-NEB / Nebulin Antibody (clone Neb-20) - LS-C171211 from LifeSpan Bioscience

Prices $295.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Anti-NEB / Nebulin Antibody - LS-C129498 from LifeSpan Bioscience

Prices $405.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal

Anti-NEB / Nebulin Antibody (clone Neb-20, Sepharose) - LS-C171213 from LifeSpan Bioscience

Prices $325.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Anti-NEB / Nebulin Antibody (clone Neb-20, Magnetic beads) - LS-C171212 from LifeSpan Bioscience

Prices $325.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Anti-NEB / Nebulin Antibody (clone 1F4) - LS-C197756 from LifeSpan Bioscience

Prices $355.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone 1F4
Detection limit for recombinant GST tagged NEB is 0.3 ng/ml as a capture antibody.

Nebulin Antibody (NB2) - NB120-11099 from Novus Biologicals

Prices $279.00
Sizes 100 µl
Host Mouse
Clonality Monoclonal
Clone NB2

Nebulin Antibody - NBP1-87752 from Novus Biologicals

Prices $419.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal

Nebulin Antibody (Neb-20) - NBP1-41355 from Novus Biologicals

Prices $329.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Nebulin Antibody (1F4) - H00004703-M01 from Novus Biologicals

Prices $359.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone 1F4
Sandwich ELISA: Nebulin Antibody (1F4) [H00004703-M01] - Detection limit for recombinant GST tagged NEB is 0.3 ng/ml as a capture antibody.

Nebulin Polyclonal Antibody - bs-2401R from Bioss

Prices $269.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal

Monoclonal Anti-NEB antibody produced in mouse - WH0004703M1 from Sigma-Aldrich

Prices $347.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone 1F4
<B>Immunoblotting</B><BR/>Monoclonal Anti-NEB, <B>Cat. No. WH0004703M1</B> used at the antibody concentration: 1 μg/mL. Specific band of ~38.21 kDa using immunogen protein lysate.

Anti-NEB antibody produced in rabbit - HPA016601 from Sigma-Aldrich

Prices $429.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal
<B>Immunohistochemistry</B><BR/>Anti-NEB: <B>Cat. No. HPA016601</B>: Immunohistochemical staining of human skeletal muscle shows cytoplasmic positivity in myocytes.

NEBULIN Antibody (OAAD00180) - OAAD00180 from Aviva Systems Biology

Prices $255.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Nebulin antibody [NB2] - GTX11099 from GeneTex

Prices $289.00
Sizes 100 μl
Host Mouse
Clonality Monoclonal
Clone NB2

Nebulin antibody - 10R-7880 from Fitzgerald

Prices $270.00
Sizes 100 µg
Host Mouse
Clonality Monoclonal
Clone Neb-20

Rabbit Anti-Nebulin Polyclonal Antibody, ALEXA FLUOR® 350 Conjugated - bs-2401R-A350 from Bioss

Prices $325.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal

Rabbit Anti-Nebulin Polyclonal Antibody, ALEXA FLUOR® 488 Conjugated - bs-2401R-A488 from Bioss

Prices $325.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal

Rabbit Anti-Nebulin Polyclonal Antibody, ALEXA FLUOR® 555 Conjugated - bs-2401R-A555 from Bioss

Prices $325.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal

Rabbit Anti-Nebulin Polyclonal Antibody, ALEXA FLUOR® 647 Conjugated - bs-2401R-A647 from Bioss

Prices $325.00
Sizes 100 µl
Host Rabbit
Clonality Polyclonal
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