Gene Symbol | RPE65 |
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Entrez Gene | 6121 |
Alt Symbol | BCO3, LCA2, RP20, mRPE65, rd12, sRPE65 |
Species | Human |
Gene Type | protein-coding |
Description | retinal pigment epithelium-specific protein 65kDa |
Other Description | BCO family, member 3|RBP-binding membrane protein|all-trans-retinyl-palmitate hydrolase|p63|retinal pigment epithelium-specific 65 kDa protein|retinitis pigmentosa 20 (autosomal recessive)|retinoid isomerohydrolase|retinol isomerase |
Swissprots | A8K1L0 Q16518 Q5T9U3 |
Accessions | AAC14586 AAC39660 ABD37636 ACT83679 AFF57192 CCQ42977 EAX06478 Q16518 AK289925 BAF82614 BC075035 AAH75035 BC075036 AAH75036 U18991 AAA99012 NM_000329 NP_000320 |
Function | Plays important roles in the production of 11-cis retinal and in visual pigment regeneration. The soluble form binds vitamin A (all-trans-retinol), making it available for LRAT processing to all-trans-retinyl ester. The membrane form, palmitoylated by LRAT, binds all-trans-retinyl esters, making them available for IMH (isomerohydrolase) processing to all-cis- retinol. The soluble form is regenerated by transferring its palmitoyl groups onto 11-cis-retinol, a reaction catalyzed by LRAT. The enzymatic activity is linearly dependent of the expression levels and membrane association. {ECO:0000269|PubMed:16116091, ECO:0000269|PubMed:21654732}. |
Subcellular Location | Cytoplasm {ECO:0000250}. Cell membrane {ECO:0000250}; Lipid-anchor {ECO:0000250}. Microsome membrane {ECO:0000250}. Note=Attached to the membrane by a lipid anchor when palmitoylated (membrane form), soluble when unpalmitoylated (By similarity). Undergoes light-dependent intracellular transport to become more concentrated in the central region of the retina pigment epithelium cells. {ECO:0000250, ECO:0000269|PubMed:21493626}. |
Tissue Specificity | Retinal pigment epithelium specific. {ECO:0000269|PubMed:21493626}. |
Top Pathways | Retinol metabolism |
Retinoid isomerohydrolase (RPE65), Human, ELISA Kit - E01R0420 from ARP American Research Products
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Chicken RPE65 ELISA Kit (Custom ELISA) - LS-F20582 from LifeSpan Bioscience
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Bovine RPE65 ELISA Kit (Custom ELISA) - LS-F20577 from LifeSpan Bioscience
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Dog RPE65 ELISA Kit (Custom ELISA) - LS-F20578 from LifeSpan Bioscience
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Rat RPE65 ELISA Kit (Custom ELISA) - LS-F20579 from LifeSpan Bioscience
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Human RPE65 ELISA Kit (Custom ELISA) - LS-F20581 from LifeSpan Bioscience
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Mouse RPE65 ELISA Kit (Custom ELISA) - LS-F20580 from LifeSpan Bioscience
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Human Retinoid isomerohydrolase ELISA Kit - abx251887 from Abbexa
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Human Retinoid isomerohydrolase ELISA Kit - EKE54298 from Biomatik
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RPE65 - EKH5032 from Nordic BioSite
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RPE65 ELISA Kit (Human) (OKEH02018) - OKEH02018 from Aviva Systems Biology
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Human RPE65 ELISA Kit - E033378 from Biobool
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Human Retinoid isomerohydrolase ELISA Kit - EK5049 from Signalway Antibody
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anti-RPE65 antibody - ARG64436 from Arigo Biolaboratories
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Retinoid isomerohydrolase, ELISA Kit - MBS9428875 from MyBioSource
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Retinoid isomerohydrolase, ELISA Kit - MBS2887655 from MyBioSource
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Human RPE65 ELISA Kit (Sandwich ELISA) - LS-F33641 from LifeSpan Bioscience
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