Gene Symbol | Mccc2 |
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Entrez Gene | 361884 |
Alt Symbol | - |
Species | Rat |
Gene Type | protein-coding |
Description | methylcrotonoyl-CoA carboxylase 2 (beta) |
Other Description | 3-methylcrotonyl-CoA carboxylase 2|3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit|3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta|MCCase subunit beta|methylcrotonoyl-CoA carboxylase beta chain, mitochondrial|methylcrotonoyl-Coenzyme A carboxylase 2 (beta) |
Swissprots | Q5XIT9 |
Accessions | Q5XIT9 BC083581 AAH83581 XM_008760678 XP_008758900 NM_001012177 NP_001012177 |
Function | Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3- methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism. {ECO:0000250}. |
Subcellular Location | Mitochondrion matrix {ECO:0000250}. |
Top Pathways | Valine, leucine and isoleucine degradation |
Recombinant Rat Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial(Mccc2) - CSB-YP726381RA CSB-EP726381RA CSB-BP726381RA CSB-MP726381RA from Cusabio
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Recombinant Rat MCCC2 Protein - MCCC2-3615R from Creative Biomart
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Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (Mccc2), Recombinant Protein - MBS1332174 from MyBioSource
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