HIBCH

Gene Symbol HIBCH
Entrez Gene 26275
Alt Symbol HIBYLCOAH
Species Human
Gene Type protein-coding
Description 3-hydroxyisobutyryl-CoA hydrolase
Other Description 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial|3-hydroxyisobutyryl-Coenzyme A hydrolase|HIB-CoA hydrolase|HIBYL-CoA-H
Swissprots Q53RF7 Q53GF2 Q53GA8 Q53TC6 D3DPI4 Q6NVY1 Q92931 Q9BS94
Accessions AAX93234 AAY24178 EAX10873 EAX10874 EAX10875 EAX10876 EAX10877 Q6NVY1 AI767349 AK126890 AK222979 BAD96699 AK223023 BAD96743 AK308042 AK313651 BC005190 AAH05190 BC067822 AAH67822 BI764401 BP193393 CA448468 CA453768 DB034438 U66669 AAC52114 XM_011510953 XP_011509255 XM_011510954 XP_011509256 XR_922903 NM_014362 NP_055177 NM_198047 NP_932164
Function Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA. {ECO:0000269|PubMed:8824301}.
Subcellular Location Mitochondrion {ECO:0000250}.
Tissue Specificity Highly expressed in liver and kidney, also detected in heart, muscle and brain (at protein level). Not detected in lung. {ECO:0000269|PubMed:8824301}.
Top Pathways Carbon metabolism, Valine, leucine and isoleucine degradation, beta-Alanine metabolism, Propanoate metabolism

HIBCH CRISPR/Cas9 KO Plasmid (h) - sc-411907 from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH HDR Plasmid (h) - sc-411907-HDR from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH Double Nickase Plasmid (h) - sc-411907-NIC from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH Double Nickase Plasmid (h2) - sc-411907-NIC-2 from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH CRISPR Activation Plasmid (h) - sc-411907-ACT from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH CRISPR Activation Plasmid (h2) - sc-411907-ACT-2 from Santa Cruz Biotechnology

Category CRISPR
Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH Lentiviral Activation Particles (h) - sc-411907-LAC from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH Lentiviral Activation Particles (h2) - sc-411907-LAC-2 from Santa Cruz Biotechnology

Prices $345.00
Sizes 20 µg
Species Reactivities Human

HIBCH siRNA (h) - sc-94322 from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

HIBCH shRNA Plasmid (h) - sc-94322-SH from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

HIBCH shRNA (h) Lentiviral Particles - sc-94322-V from Santa Cruz Biotechnology

Category siRNA
Prices $258.00
Sizes 10 µm
Species Reactivities Human

MISSION® esiRNA - EHU091771 from Sigma-Aldrich

Category siRNA
Prices $140.00, $250.00
Sizes 20 µg, 50 µg

CompoZr® Knockout ZFN Kit - CKOZFN10028 from Sigma-Aldrich

Category ZFN Kit
Prices $4,999.00
Sizes 1 kt

CompoZr® Knockout ZFN Kit, ZFN plasmid only - CKOZFND10028 from Sigma-Aldrich

Category ZFN Kit
Prices $3,999.00
Sizes 1 kt

MISSION® 3′UTR Lenti GoClone™ - HUTR06753 from Sigma-Aldrich

Category miRNA

HIBCH siRNA (Human) - CRH8797 from Cohesion Biosciences

Category siRNA
Prices $340.00, $510.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

HIBCH - MBS8239535 from MyBioSource

Prices $365.00, $515.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

shRNA set against Human HIBCH (NM_198047.2) - SHH312081 from Creative biogene

Category siRNA
Species Reactivities Human

Human HIBCH siRNA - orb269299 from Biorbyt

Category siRNA
Prices $485.00, $629.00
Sizes 15 nmol, 30 nmol
Species Reactivities Human

HIBCH shRNA Plasmid (Human) - CHH8797 from Cohesion Biosciences

Category siRNA
Prices $500.00, $750.00
Sizes 150 µg, 300 µg
Species Reactivities Human

HIBCH miRNA 3'UTR clone - MiUTR3H-11413 from Creative biogene

Species Reactivities Human

HIBCH miRNA 3'UTR clone - MiUTR3H-11414 from Creative biogene

Species Reactivities Human
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