Gene Symbol | HSD17B10 |
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Entrez Gene | 3028 |
Alt Symbol | 17b-HSD10, ABAD, CAMR, DUPXp11.22, ERAB, HADH2, HCD2, MHBD, MRPP2, MRX17, MRX31, MRXS10, SCHAD, SDR5C1 |
Species | Human |
Gene Type | protein-coding |
Description | hydroxysteroid (17-beta) dehydrogenase 10 |
Other Description | 3-hydroxy-2-methylbutyryl-CoA dehydrogenase|3-hydroxyacyl-CoA dehydrogenase type-2|AB-binding alcohol dehydrogenase|amyloid-beta peptide binding alcohol dehydrogenase|endoplasmic reticulum-associated amyloid beta-peptide-binding protein|mitochondrial RNase P subunit 2|mitochondrial ribonuclease P protein 2|short chain L-3-hydroxyacyl-CoA dehydrogenase type 2|short chain dehydrogenase/reductase family 5C member 1|short chain dehydrogenase/reductase family 5C, member 1|short chain type dehydrogenase/reductase XH98G2 |
Swissprots | Q8TCV9 Q5H927 Q6IBS9 Q99714 Q96HD5 |
Accessions | AAC16419 ABC70292 CAI42651 CAI42652 CAI42653 EAW93157 EAW93158 EAW93159 Q99714 AF035555 AAC15902 AF069134 AAC39900 AU132847 AY092415 AAM18189 BC000372 AAH00372 BC000829 BC008708 AAH08708 CR456723 CAG33004 JF432473 ADZ15690 U73514 AAB68958 U96132 AAC51812 NM_001037811 NP_001032900 NM_004493 NP_004484 |
Function | Functions in mitochondrial tRNA maturation. Part of mitochondrial ribonuclease P, an enzyme composed of MRPP1/TRMT10C, MRPP2/HSD17B10 and MRPP3/KIAA0391, which cleaves tRNA molecules in their 5'-ends. Catalyzes the beta-oxidation at position 17 of androgens and estrogens and has 3-alpha-hydroxysteroid dehydrogenase activity with androsterone. Catalyzes the third step in the beta-oxidation of fatty acids. Carries out oxidative conversions of 7-alpha-OH and 7-beta-OH bile acids. Also exhibits 20-beta-OH and 21-OH dehydrogenase activities with C21 steroids. By interacting with intracellular amyloid-beta, it may contribute to the neuronal dysfunction associated with Alzheimer disease (AD). {ECO:0000269|PubMed:12917011, ECO:0000269|PubMed:18984158, ECO:0000269|PubMed:9338779}. |
Subcellular Location | Mitochondrion {ECO:0000269|PubMed:12917011, ECO:0000269|PubMed:18984158}. |
Tissue Specificity | Ubiquitously expressed in normal tissues but is overexpressed in neurons affected in AD. {ECO:0000269|PubMed:9338779}. |
Top Pathways | Alzheimer's disease, Valine, leucine and isoleucine degradation |
ERAB CRISPR/Cas9 KO Plasmid (h) - sc-405211 from Santa Cruz Biotechnology
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ERAB HDR Plasmid (h) - sc-405211-HDR from Santa Cruz Biotechnology
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ERAB Double Nickase Plasmid (h) - sc-405211-NIC from Santa Cruz Biotechnology
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ERAB Double Nickase Plasmid (h2) - sc-405211-NIC-2 from Santa Cruz Biotechnology
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ERAB CRISPR Activation Plasmid (h) - sc-405211-ACT from Santa Cruz Biotechnology
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ERAB CRISPR Activation Plasmid (h2) - sc-405211-ACT-2 from Santa Cruz Biotechnology
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ERAB Lentiviral Activation Particles (h) - sc-405211-LAC from Santa Cruz Biotechnology
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ERAB Lentiviral Activation Particles (h2) - sc-405211-LAC-2 from Santa Cruz Biotechnology
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ERAB siRNA (h) - sc-41938 from Santa Cruz Biotechnology
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ERAB shRNA Plasmid (h) - sc-41938-SH from Santa Cruz Biotechnology
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ERAB shRNA (h) Lentiviral Particles - sc-41938-V from Santa Cruz Biotechnology
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ERAB RNAi - H00003028-R02 from Novus Biologicals
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MISSION® esiRNA - EHU015171 from Sigma-Aldrich
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CompoZr® Knockout ZFN Kit - CKOZFN10322 from Sigma-Aldrich
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CompoZr® Knockout ZFN Kit, ZFN plasmid only - CKOZFND10322 from Sigma-Aldrich
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HSD17B10 siRNA (Human) - CRH2057 from Cohesion Biosciences
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ERAB RNAi - H00003028-R01 from Novus Biologicals
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HSD17B10 - MBS8235603 from MyBioSource
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shRNA set against Human HSD17B10 (NM_004493.2) - SHH315145 from Creative biogene
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shRNA set against Human HSD17B10(NM_001037811.2) - SHH132411 from Creative biogene
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shRNA set against Human HSD17B10(NM_004493.2) - SHH132429 from Creative biogene
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HSD17B10 shRNA Plasmid (Human) - CHH2057 from Cohesion Biosciences
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HSD17B10 miRNA 3'UTR clone - MiUTR1H-04712 from Creative biogene
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HSD17B10 miRNA 3'UTR clone - MiUTR1H-04713 from Creative biogene
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